29505-5  2-Hydroxy-3-Methylvalerate/​Creatinine [Molar ratio] in Urine2-Hydroxy-3-Methylvalerate/​Creatinine [Molar ratio] in Urine2-Hydroxy-3-Methylvalerate/​Creatinine: SRto: Pt: Urine: Qn:  

NAME
  Fully Specified Name: 
Component   Property   Time   System   Scale   Method
2-Hydroxy-3-Methylvalerate/Creatinine  SRto  Pt  Urine  Qn 
  Long Common Name:  2-Hydroxy-3-Methylvalerate/Creatinine [Molar ratio] in Urine
  Short Name:  2OH3Me-valerate/Creat Ur-sRto
  Display Name:  2-Hydroxy-3-Methylvalerate/Creatinine (U) [Molar ratio]

PART DEFINITION/DESCRIPTION(S)
  Part: 2-Hydroxy-3-Methylvalerate
  2-hydroxy-3-methylvaleric acid (HMVA) is an acid generated by L-isoleucine oxidation pathway and involves four stereoisomers (2S,3S-HMVA, 2R,3R-HMVA, 2S,3R-HMVA and 2R,3S-HMVA). Increased levels of HMVA are found in patients with maple syrup urine disease (MSUD), an inherited metabolic disease characterized by sweet-smelling urine, ketoacidosis, seizures, and neurological dysfunction.
 
 

BASIC ATTRIBUTES
  Class/Type: CHEM/Lab
  First Released in Version: 2.03
  Last Updated in Version: 2.42
  Mass or Substance Property: S
  Order vs. Obs.: Observation
  Status: Active

SUBMITTER'S INFORMATION
  Submitted Units: mmol/mol cr

MEMBER OF THESE PANELS     
  This section provides information about panels that contain this LOINC code.
  LOINC   Long Common Name  
  48797-5 Organic acids panel - Urine
  

MEMBER OF THESE EQUIVALENCE GROUPS
  LG35765-3  2-Hydroxy-3-Methylvalerate/Creatinine|SRto|Urine

PARTS

Part Type    Part No.  Part Name   
Component   LP18400-9  2-Hydroxy-3-Methylvalerate 
     Divisors   LP32035-5  Creatinine 
Property   LP6868-6  SRto   [Substance Ratio] 
Time   LP6960-1  Pt   [Point in time (spot)] 
System   LP7681-2  Urine 
Scale   LP7753-9  Qn 
Fragments for synonyms   LP20740-4 
Fragments for synonyms   LP20785-9  Hydroxy 
Fragments for synonyms   LP21267-7 

LANGUAGE VARIANTS
  Chinese (CHINA)  (From: Regenstrief-generated full translation based on part translation provided by Lin Zhang, A LOINC volunteer from China)
 
  2-羟基-3-甲基戊酸/​肌酐:物质的量比率:时间点:尿液:定量型:2-羟基-3-甲基戊酸/​肌酐:物质的量比率:时间点:尿液:定量型:
  Dutch (NETHERLANDS)  (From: Regenstrief-generated full translation based on part translation provided by NVKC, Dutch Society for Clinical Chemistry and Laboratory Medicine, The Netherlands)
 
  2-hydroxy-3-methylvaleraat/​creatinine:molaire verhouding:moment:urine:kwantitatief:2-hydroxy-3-methylvaleraat/​creatinine:molaire verhouding:moment:urine:kwantitatief:
  French (BELGIUM)  (From: Regenstrief-generated full translation based on part translation provided by Jean M. Prevost, MD, Biopathology)
 
  2-hydroxy-3-méthylvalérate/​Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:2-hydroxy-3-méthylvalérate/​Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
  French (CANADA)  (From: Regenstrief-generated full translation based on part translation provided by Canada Health Infoway Inc.)
 
  2-hydroxy-3-méthylvalérate/​Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:2-hydroxy-3-méthylvalérate/​Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
  French (FRANCE)  (From: ASIP Santé (Agence des systèmes d'information partagés de santé))
 
  2-Hydroxy-3-Methylvalerate/​Creatinine:SRto:Pt:Urine:Qn:2-Hydroxy-3-Methylvalerate/​Creatinine:SRto:Pt:Urine:Qn:2-hydroxy-3-méthylvalérate/​créatinine [Moles ratio] Urine ; Numérique
  German (GERMANY)  (From: Institute for Medical Documentation and Information (DIMDI))
 
  2-Hydroxy-3-Methylvalerat/​Kreatinin:SKRto:Pkt:Urin:Qn:2-Hydroxy-3-Methylvalerat/​Kreatinin:SKRto:Pkt:Urin:Qn:
  Italian (ITALY)  (From: Regenstrief-generated full translation based on part translation provided by Consiglio Nazionale delle Ricerche)
 
  2-Idrossi-3-Metilvalerato/​Creatinina:Srto:Pt:Urine:Qn:2-Idrossi-3-Metilvalerato/​Creatinina:Srto:Pt:Urine:Qn:
  Korean (KOREA, REPUBLIC OF)  (From: Korean Ministry for Health, Welfare, and Family Affairs)
 
  2-하이드록시-3-메틸발레레이트/​크레아티닌:물질구성비:검사시점:뇨:정량:2-하이드록시-3-메틸발레레이트/​크레아티닌:물질구성비:검사시점:뇨:정량:
  Portuguese (BRAZIL)  (From: HL7 Brazil Institute)
 
  2-Hidroxi-3-Metilvalerato/​Creatinina:SCrto:Pt:Urina:Qn:2-Hidroxi-3-Metilvalerato/​Creatinina:SCrto:Pt:Urina:Qn:
  Russian (RUSSIAN FEDERATION)  (From: Regenstrief-generated full translation based on part translation provided by Yaroslavl State Medical Academy)
 
  2-Гидрокси-3-Метилвалерат/​Креатинин:МольОтн:ТчкВрм:Моча:Колич:2-Гидрокси-3-Метилвалерат/​Креатинин:МольОтн:ТчкВрм:Моча:Колич:
  Spanish (ARGENTINA)  (From: Conceptum Medical Terminology Center)
 
  2-hidroxi-3-metilvalerato/​creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:2-hidroxi-3-metilvalerato/​creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
  Spanish (SPAIN)  (From: Regenstrief-generated full translation based on part translation provided by the Clinical Laboratory Committee of SERVICIO EXTREMEÑO DE SALUD, with the support of BITAC MAP.)
 
  2-Hidroxi-3-Metilvalerato/​Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:2-Hidroxi-3-Metilvalerato/​Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
  Turkish (TURKEY)  (From: Regenstrief-generated full translation based on part translation provided by LOINC Turkish Translation Group and the Turkish Ministry of Health)
 
  2-Hidroksi-3-Metilvalerat/​Kreatinin:SOrn:Zmlı:İdrar:Kant:2-Hidroksi-3-Metilvalerat/​Kreatinin:SOrn:Zmlı:İdrar:Kant:

RELATED NAMES
  2-Hydroxy-3-Methyl valerate II Scrto
  2-hydroxy-3-methylvaleric acid III Substance concentration ratio
  2OH3Me-valerate OH Substance ratio
  Chemistry Point in time UA
  CR QNT UCr
  Crea Quan UR
  Creat Quant Urn
  HMVA Quantitative  
  Hydrox Random  

EXAMPLE UNITS
  Unit  Source Type
  mmol/mol cr  ORIGINAL SUBMISSION 
  mmol/mol cr  REGENSTRIEF 
  mmol/mol{creat}  EXAMPLE UCUM UNITS 

UNITS (INTERNAL DETAILS)
  Source Type:  ORIGINAL SUBMISSION 
  Unit:  mmol/mol cr 
  Source Type:  REGENSTRIEF 
  Unit:  mmol/mol cr 
  Source Type:  EXAMPLE UCUM UNITS 
  Unit:  mmol/mol{creat} 

CHANGE HISTORY
  Change Type: MIN

INTERNAL FIELDS
  Detail Page Created On: 6/26/2019 6:40:23 PM
  Attachment Units Required: N
  Long Common Name: 2-Hydroxy-3-Methylvalerate/Creatinine [Molar ratio] in Urine
  Shortname: 2OH3Me-valerate/Creat Ur-sRto
  Fully Specified Name: 2-Hydroxy-3-Methylvalerate/Creatinine: SRto: Pt: Urine: Qn:
     
  Component Word Count: 5
  ID: 21281
  Status (Raw): ACTIVE